Granulomatous slack skin: a distinct disorder or a variant of mycosis fungoides?

نویسندگان

  • G Topar
  • B Zelger
  • M Schmuth
  • N Romani
  • J Thaler
  • N Sepp
چکیده

About 75% of cutaneous lymphomas belong to the group of T-cell lymphomas. Mycosis fungoides is the most common entity in this group. Granulomatous slack skin is a rare form of cutaneous T-cell lymphoma closely related to mycosis fungoides. We present here a patient with areas of lax skin for several years who developed a generalized erythroderma with associated immunoactivation and a deterioration in his general condition. This report discusses clinically and histologically the differential diagnoses, namely granulomatous slack skin and granulomatous mycosis fungoides, and suggests that these 2 disorders are only variants in the broad spectrum of a single disease.

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عنوان ژورنال:
  • Acta dermato-venereologica

دوره 81 1  شماره 

صفحات  -

تاریخ انتشار 2001